Vietnamese Journal of Neurology

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Tổng quan Issue: Số 33 - 2022 Bệnh thần kinh - cơ

Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP): Diagnostic Pitfalls and Therapeutic Approaches

Published: June 15, 2022
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Abstract

Chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) is an immune-mediated peripheral neuropathy characterized by progressive muscle weakness, sensory impairment, and diminished or absent deep tendon reflexes. This review summarizes current diagnostic criteria, clinical variants, common diagnostic pitfalls, and important differential diagnoses of CIDP. It discusses the roles of nerve conduction studies, cerebrospinal fluid analysis, magnetic resonance imaging, nerve ultrasound, and nerve biopsy in supporting the diagnosis. The article also reviews current treatment strategies, including intravenous immunoglobulin, subcutaneous immunoglobulin, corticosteroids, plasma exchange, and therapeutic approaches for refractory disease, emphasizing individualized treatment and objective monitoring of treatment response.

Keywords
Chronic inflammatory demyelinating polyradiculoneuropathy CIDP Diagnosis Immunotherapy

Authors

Amro M. Stino MD Đại học Y khoa Michigan Elie Naddaf MD Mayo Clinic Peter J. Dyck MD Mayo Clinic Nguyễn Hải Anh Bệnh viện Bạch Mai, Đại học Y Dược Đại học Quốc gia Hà Nội

Trung tâm Thần kinh Bệnh viện Bạch Mai
Bộ môn Thần kinh, Đại học Y Dược Đại học Quốc gia Hà Nội

Đinh Thị Lợi Bệnh viện Bạch Mai
Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP): Diagnostic Pitfalls and Therapeutic Approaches

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Section Tổng quan
Category Bệnh thần kinh - cơ
Pages 78-92
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